Inmunodeficiencia mixta grave. Presentacióm de un caso

R. Santana Mondragón*, J. Ramírez Mayans, R. Berrón Pérez, C. Ridaura Sanz, G. López Cervantes

*Autor correspondiente de este trabajo

Producción científica: Contribución a una revistaArtículorevisión exhaustiva

Resumen

The case of a 3 month old child with severe combined sex linked immunodeficiency is presented. The diagnosis was well doccumented, during his life. The child presented as a case of mucocutaneous moniliasis resistant to treatment. There was a history of similar cases in the family; diagnosis was made at post-mortem in one cousin and death occurred at early age in all kins so affected. Blood marrow transplant was not feasible in our case because histocompatibility was lacking in the kins studied. Three units of transfer factor were given as well as hyperimmune plasma but the child died in respiratory failure. Autopsy demonstrated pulmonary infection by Pneumocystic carinii and generalized citomegalic inclussion virus infection; almost complete absence of immune tissue was also demonstrated.

Título traducido de la contribuciónSevere mixed immunodeficiency. Report of a case
Idioma originalEspañol
Páginas (desde-hasta)1033-1045
Número de páginas13
PublicaciónBoletin Medico del Hospital Infantil de Mexico
Volumen32
N.º6
EstadoPublicada - nov. 1975

Huella

Profundice en los temas de investigación de 'Inmunodeficiencia mixta grave. Presentacióm de un caso'. En conjunto forman una huella única.

Citar esto